Recommendations for Managing Adults With Histiocytic Neoplasms: New NCCN Guidelines

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Ronald S. Go
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Volume/Issue:
Volume 19: Issue 11.5
Online Publication Date:
Nov 2021
DOI:
https://doi.org/10.6004/jnccn.2021.5103
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The histiocytoses, a group of clonal and reactive conditions, arise from monocytic macrophage or dendritic cell lineages. The current NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines) for Histiocytic Neoplasms reflect the most up-to-date, evidence-based data relating to the evaluation and management of this disease. Specifically, the guidelines focus on adult Langerhans cell histiocytosis, Erdheim-Chester disease, and Rosai-Dorfman disease. Because these disorders are rare, challenges have arisen regarding clinical suspicion, histologic diagnosis, treatment, and molecular subtyping. Future versions of the NCCN Guidelines will address the diagnosis and management of pediatric patients, as well as malignant histiocytosis.

Disclosures: Dr. Go has disclosed having no relevant financial relationships.

Correspondence: Ronald S. Go, MD, Mayo Clinic Cancer Center, 200 First Street SW, Rochester, MN 55905. Email: Go.Ronald@mayo.edu
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Print ISSN:
1540-1405
Online ISSN:
1540-1413
Publisher:
National Comprehensive Cancer Network
Cover Journal of the National Comprehensive Cancer Network
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  • 8.

    Go RS, Jacobsen E, Baiocchi R, et al. NCCN Clinical Practice Guidelines in Oncology: Histiocytic Neoplasms. Version 2. 2021. Accessed September 21, 2021. To view the most recent version, visit NCCN.org

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Copyright:
Copyright © 2021 by the National Comprehensive Cancer Network 2021
Page Numbers:
3
Article Category:
Research Article
Print Publication Date:
Nov 2021
Online Publication Date:
Nov 2021

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